Unilateral pulmonary artery agenesis diagnosed in adulthood: a case report
نویسندگان
چکیده
Isolated pulmonary artery agenesis (UPAA) diagnosed in adulthood is a rare congenital anomaly. It occurs during embryological development where there fusion failure between sixth aortic arch and truck of affected side. Here we report case an adult patient with isolated unilateral right aplasia.
منابع مشابه
Unilateral pulmonary artery agenesis: a case series.
BACKGROUND Unilateral pulmonary artery agenesis (UPAA) is a rare congenital anomaly due to a malformation of the sixth aortic arch of the affected side during embryogenesis. The diagnosis is usually set at adolescence, however it can remain asymptomatic and late diagnosis is possible. DESCRIPTION We present a case series of three female patients, aged 18, 49 and 68 years old, with history of ...
متن کاملUnilateral pulmonary agenesis presenting in adulthood
Agenesis of lung,a rare congenital anomaly,may present in adult life with features of recurrent chest infections and radiologically may mimic many common conditions presenting as opaque hemithorax with ipsilateral shifting of mediastinum.Here, a case of a young man presenting with frequent attacks of cough expectoration and progressive dyspnoea since childhood,proved to be a case of left pulmon...
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A 33-year-old woman with a history of psoriasis presented with asymmetric oligoarthritis. She had no cardiovascular symptoms. Naproxen and steroids were started with the diagnosis of psoriatic arthritis. Routine chest X-ray showed a small left hemithorax with a right-sided aortic arch and decreased left-sided pulmonary vasculature. A CTscan (Picture A) demonstrated the absence of the left pulmo...
متن کاملUnilateral Pulmonary Artery Agenesis in an Adult Patient with Cough and Hemoptysis: A Case Report
Unilateral pulmonary artery agenesis (UPAA) is an uncommon congenital anomaly and most patients present in neonatal period with respiratory symptoms. Left-sided pulmonary artery agenesis is less frequent than right-sided and is sometimes associated with cardiac anomalies. We report a patient with a history of repaired ventricular septal defect, who presented with cough and hemoptysis and the di...
متن کاملImaging features of isolated unilateral pulmonary artery agenesis presenting in adulthood: a review of four cases.
AIM To highlight the variation in clinical manifestations, imaging and management of four cases of unilateral pulmonary artery agenesis presenting in adulthood. METHOD Four patients with unilateral pulmonary artery agenesis were referred to our institution between 1995 and 2005. They underwent a series of investigations, including chest radiography, echocardiography, ventilation perfusion sci...
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ژورنال
عنوان ژورنال: International Journal of Advances in Medicine
سال: 2023
ISSN: ['2349-3925', '2349-3933']
DOI: https://doi.org/10.18203/2349-3933.ijam20231027